|
KMID : 0364020070400040297
|
|
Korean Journal of Thoracic and Cardiovascular Surgery
2007 Volume.40 No. 4 p.297 ~ p.300
|
|
|
Dysfunction of the Prosthetic Aortic Valve in Idiopathic Hypereosinophilic Syndrome -A case report-
|
|
Park Chong-Bin
Yoo Dong-Gon
Seong Kyu-Wan
Jung Sang-Sig
Kang Gil-Hyun
Kim Chong-Wook
|
|
|
Abstract
|
|
|
|
Idiopathic hypereosinophilic syndrome is a rare systemic, leukoproliferative disorder characterized by eosinophil- mediated tissue injury causing multiple organ failure, including the heart. Cardiac involvement occurs in more than 75% of patients with hypereosinophilic syndrome. Cardiac manifestations include subendocardial fibrosis, thrombus leading to peripheral emboli, restrictive cardiomyopathy, and valvular dysfunction. It is more common in men than in women (9：1), and trends to present between the ages of 20 and 50 years. Presentation in childhood is unusual. We report for the first time a case of a 58-year-old man with idiopathic hypereosinophilic syndrome manifested by prosthetic aortic valve dysfunction that was successfully treated by steroid and hydroxyurea therapy after surgical valvular replacement.
|
|
|
KEYWORD
|
|
|
Hypereosinophilic syndrome, idiopathic, Aortic valve, surgery
|
|
|
FullTexts / Linksout information
|
|
 
|
|
|
Listed journal information
|
|
  
|